A portion of amino acids 1-30 from the human protein was used as the immunogen for this ACOX2 antibody.
Peroxisomal acyl-coenzyme A oxidase 2 belongs to the acyl-CoA oxidase family. It encodes the branched-chain acyl-CoA oxidase which is involved in the degradation of long branched fatty acids and bile acid intermediates in peroxisomes. Deficiency of this enzyme results in the accumulation of branched fatty acids and bile acid intermediates, and may lead to Zellweger syndrome, severe mental retardation, and death in children.
