FH Polyclonal Antibody, AbBy Fluor-594 Conjugated, BF594, Rabbit

Produktübersicht

• Artikelname: FH Polyclonal Antibody, AbBy Fluor-594 Conjugated, BF594, Rabbit
• Artikelnummer: BSS-BS-3938R-BF594
• Hersteller Artikelnummer: bs-3938R-BF594
• Alternativnummer: BSS-BS-3938R-BF594-100
• Hersteller: Bioss
• Wirt: Rabbit
• Kategorie: Antikörper
• Applikation: IF
• Spezies Reaktivität: Mouse, Rat
• Konjugation: BF594
• Alternative Synonym: mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.

Produktbeschreibung

Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.

Produkteigenschaften

• Klonalität: Polyclonal
• Konzentration: 1ug/ul
• NCBI: 2271
• Puffer: Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
• Quelle: KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
• Target-Kategorie: FH

Anwendungsbeschreibung

• Application Verdünnung: IF(IHC-P)(1:50-200), IF(IHC-F)(1:50-200), IF(ICC)(1:50-200)