FH Polyclonal Antibody, PerCP-Cy5.5 Conjugated, PerCP/Cy5.5, Rabbit
Artikelnummer:
BSS-BS-3938R-PERCP-CY5.5
Produktübersicht
Artikelname:
FH Polyclonal Antibody, PerCP-Cy5.5 Conjugated, PerCP/Cy5.5, Rabbit
Artikelnummer:
BSS-BS-3938R-PERCP-CY5.5
Hersteller Artikelnummer:
bs-3938R-PerCP-Cy5.5
Alternativnummer:
BSS-BS-3938R-PERCP-CY5.5-100
Hersteller:
Bioss
Wirt:
Rabbit
Kategorie:
Antikörper
Applikation:
IF
Spezies Reaktivität:
Mouse, Rat
Konjugation:
PerCP/Cy5.5
Alternative Synonym:
mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.
Produktbeschreibung
Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
Produkteigenschaften
Klonalität:
Polyclonal
Konzentration:
1ug/ul
NCBI:
2271
Puffer:
Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
Quelle:
KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
Target-Kategorie:
FH
Anwendungsbeschreibung
Application Verdünnung:
IF(IHC-P)(1:50-200), IF(IHC-F)(1:50-200), IF(ICC)(1:50-200)
