ECHS 1, Enoyl CoA hydratase 1, Enoyl CoA hydratase mitochondrial, Enoyl CoA hydratase short chain 1 mitochondrial, Enoyl Coenzyme A hydratase short chain 1, Enoyl Coenzyme A hydratase short chain 1 mitochondrial, Mitochondrial short chain enoyl coenzyme A hydratase 1, OTTHUMP00000020811, SCEH, Short chain enoyl CoA hydratase, C80529, EC 4.2.1.17.
ECHS1 (Enoyl Coenzyme A hydratase, short chain, 1) catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs, in the second step of the mitochondrial fatty acid beta-oxidation pathway.