Glutarylcarnitine lithium is a crucial biomarker for diagnosing malonic aciduria and glutaric aciduria type I, widely employed in newborn screening via tandem mass spectrometry. This compound is utilized in research applications, including in vitro assays and metabolic disorder studies, to investigate fatty acid oxidation and organic acidemias.
Molekulargewicht:
281.23
Formel:
C12H20LiNO6
Target-Kategorie:
Endogenous Metabolite,Others
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