SGSH Protein, Human, Recombinant (His)

Produktübersicht

• Artikelname: SGSH Protein, Human, Recombinant (His)
• Artikelnummer: TGM-TMPJ-01002
• Hersteller Artikelnummer: TMPJ-01002
• Alternativnummer: TGM-TMPJ-01002-1MG,TGM-TMPJ-01002-5UG,TGM-TMPJ-01002-10UG,TGM-TMPJ-01002-20UG,TGM-TMPJ-01002-50UG,TGM-TMPJ-01002-100UG,TGM-TMPJ-01002-200UG,TGM-TMPJ-01002-500UG
• Hersteller: TargetMol
• Kategorie: Biochemikalien
• Alternative Synonym: SGSH , N-Sulphoglucosamine Sulphohydrolase , Sulfoglucosamine Sulfamidase , Sulphamidase , HSS

Produktbeschreibung

N-Sulphoglucosamine Sulphohydrolase (SGSH) is an important member of the sulfatase family which is involved in the degradation of heparin sulfate. SGSH binds one calcium ion per subunit as a cofactor. SGSH catalyzes N-sulfo-D-glucosamine and H2O to D-glucosamine and sulfate. SGSH deficiency is result in mucopolysaccharidosis type 3A (MPS3A), a recessive lysosomal storage disease characterized by neurological dysfunction but relatively mild somatic manifestations.

Bilder

TMPJ-01002