UPB1 Protein, Human, Recombinant (His)

Produktübersicht

• Artikelname: UPB1 Protein, Human, Recombinant (His)
• Artikelnummer: TGM-TMPJ-01374
• Hersteller Artikelnummer: TMPJ-01374
• Alternativnummer: TGM-TMPJ-01374-1MG,TGM-TMPJ-01374-5UG,TGM-TMPJ-01374-10UG,TGM-TMPJ-01374-20UG,TGM-TMPJ-01374-50UG,TGM-TMPJ-01374-100UG,TGM-TMPJ-01374-200UG,TGM-TMPJ-01374-500UG
• Hersteller: TargetMol
• Kategorie: Biochemikalien
• Alternative Synonym: beta-Ureidopropionase , Beta-Alanine Synthase , beta-Alanine Synthase , BUP1 , UPB1 , N-Carbamoyl-beta-Alanine Amidohydrolase , Beta-Ureidopropionase , N-Carbamoyl-Beta-Alanine Amidohydrolase , BUP-1

Produktbeschreibung

beta-Ureidopropionase is a cytoplasmic protein which belongs to the CN hydrolase family of BUP subfamily. beta-Ureidopropionase binds one zinc ion per subunit, catalyzes the last step in the pyrimidine degradation pathway. beta-Ureidopropionase can convert N-carbamyl-beta-aminoisobutyric acid and N-carbamyl-beta-alanine to beta-aminoisobutyric acid and beta-alanine, ammonia and carbon dioxide, respectively. The pyrimidine bases uracil and thymine are degraded via the consecutive action of dihydropyrimidine dehydrogenase (DHPDH), dihydropyrimidinase (DHP) and beta-ureidopropionase (UP) to beta-alanine and beta aminoisobutyric acid, respectively. Defects in beta-Ureidopropionase are the cause of beta-Ureidopropionase deficiency that is characterized by muscular hypotonia, dystonic movements, scoliosis, microcephaly and severe developmental delay.

Bilder

TMPJ-01374