GBA Rabbit monoclonal antibody, Unconjugated
Artikelnummer:
BWT-BS40462
Produktübersicht
Artikelname:
GBA Rabbit monoclonal antibody, Unconjugated
Artikelnummer:
BWT-BS40462
Hersteller Artikelnummer:
BS40462
Alternativnummer:
BWT-BS40462-50UL,BWT-BS40462-100UL
Hersteller:
Bioworld Technology
Wirt:
Rabbit
Kategorie:
Antikörper
Applikation:
IHC, WB
Spezies Reaktivität:
Human, Rat
Immunogen:
A synthesized peptide derived from human GBA
Konjugation:
Unconjugated
Alternative Synonym:
Alglucerase, betaGC, GBA1, GCase, GCB, GLUC, Glucosylceramidase, Imiglucerase,
Produktbeschreibung
Defects in GBA are the cause of Gaucher disease (GD) [MIM:230800], also known as glucocerebrosidase deficiency. GD is the most prevalent lysosomal storage disease, characterized by accumulation of glucosylceramide in the reticulo-endothelial system.
Produkteigenschaften
Molekulargewicht:
60kDa
UniProt:
P04062
Reinheit:
Affinity-chromatography
Formulierung:
Rabbit IgG, 1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.2.
Anwendungsbeschreibung
Application Verdünnung:
WB 1:500~1:2000 IHC 1:50~1:200
Anwendungsbeschreibung:
GBA Antibody detects endogenous levels of total GBA
