GBA Rabbit monoclonal antibody, Unconjugated
Catalog Number:
BWT-BS40462
Product Overview
Article Name:
GBA Rabbit monoclonal antibody, Unconjugated
Biozol Catalog Number:
BWT-BS40462
Supplier Catalog Number:
BS40462
Alternative Catalog Number:
BWT-BS40462-50UL,BWT-BS40462-100UL
Manufacturer:
Bioworld Technology
Host:
Rabbit
Category:
Antikörper
Application:
IHC, WB
Species Reactivity:
Human, Rat
Immunogen:
A synthesized peptide derived from human GBA
Conjugation:
Unconjugated
Alternative Names:
Alglucerase, betaGC, GBA1, GCase, GCB, GLUC, Glucosylceramidase, Imiglucerase,
Product Description
Defects in GBA are the cause of Gaucher disease (GD) [MIM:230800], also known as glucocerebrosidase deficiency. GD is the most prevalent lysosomal storage disease, characterized by accumulation of glucosylceramide in the reticulo-endothelial system.
Product Properties
Molecular Weight:
60kDa
UniProt:
P04062
Purity:
Affinity-chromatography
Form:
Rabbit IgG, 1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.2.
Application Notes
Application Dilute:
WB 1:500~1:2000 IHC 1:50~1:200
Application Notes:
GBA Antibody detects endogenous levels of total GBA
