Glutaryl-L-Carnitine, Lithium Salt, CAS [[102636-82-8 free acid]]

Artikelnummer: USB-376887
Artikelname: Glutaryl-L-Carnitine, Lithium Salt, CAS [[102636-82-8 free acid]]
Artikelnummer: USB-376887
Hersteller Artikelnummer: 376887
Alternativnummer: USB-376887-10
Hersteller: US Biological
Kategorie: Biochemikalien
A metabolite of L-Carnitine. Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction. Optical Activity: 20/D -202, c = 1 in H2O Impurities: 10% water Storage and Stability: Store at 4C. Stable for 6 months after receipt. For maximum recovery of product, centrifuge the original vial prior to removing the cap. Hygroscopic. Store under inert atmosphere.
Molekulargewicht: 275.3
Reinheit: 98% (TLC)
Formulierung: Supplied as a white to off-white powder or crystals.
CAS Nummer: [102636-82-8 free acid]