Glutaryl-L-Carnitine, Lithium Salt, CAS [[102636-82-8 free acid]]

Catalog Number: USB-376887
Article Name: Glutaryl-L-Carnitine, Lithium Salt, CAS [[102636-82-8 free acid]]
Biozol Catalog Number: USB-376887
Supplier Catalog Number: 376887
Alternative Catalog Number: USB-376887-10
Manufacturer: US Biological
Category: Biochemikalien
A metabolite of L-Carnitine. Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction. Optical Activity: 20/D -202, c = 1 in H2O Impurities: 10% water Storage and Stability: Store at 4C. Stable for 6 months after receipt. For maximum recovery of product, centrifuge the original vial prior to removing the cap. Hygroscopic. Store under inert atmosphere.
Molecular Weight: 275.3
Purity: 98% (TLC)
Form: Supplied as a white to off-white powder or crystals.
CAS Number: [102636-82-8 free acid]