SGSH Antibody - N-terminal region

Product Overview

• Article Name: SGSH Antibody - N-terminal region
• Biozol Catalog Number: ASB-ARP48123_P050
• Supplier Catalog Number: ARP48123_P050
• Alternative Catalog Number: ASB-ARP48123_P050-25UL,ASB-ARP48123_P050-100UL
• Manufacturer: Aviva
• Host: Rabbit
• Category: Proteine/Peptide
• Application: WB
• Species Reactivity: Bovine, Canine, Equine, Guinea pig, Human, Mouse, Porcine, Rat
• Immunogen: The immunogen is a synthetic peptide directed towards the N-terminal region of Human SGSH
• Alternative Names: HSS, SFMD, MPS3A

Product Description

This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.

Product Properties

• Clonality: Polyclonal
• Concentration: 0.5 mg/ml
• Molecular Weight: 57kDa
• NCBI: 6448
• UniProt: P51688
• Form: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09% (w/v) sodium azide and 2% sucrose.

Images

Host: Rabbit
Target Name: SGSH
Sample Type: 721_B Whole Cell lysates
Antibody Dilution: 1.0ug/mlSGSH is supported by BioGPS gene expression data to be expressed in 721_B

Host: Rabbit
Target Name: SGSH
Sample Tissue: Human THP-1 Whole Cell
Antibody Dilution: 1ug/ml

Host: Rabbit
Target Name: SGSH
Sample Tissue: Human A549 Whole Cell
Antibody Dilution: 1ug/ml

SGSH Antibody - N-terminal region (ARP48123_P050) in Human 721_B using Western Blot