Pyruvate Dehydrogenase E2, 70 kDa mitochondrial autoantigen of primary biliary cirrhosis, anti DLAT, Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex, Dihydrolipoamide, Dihydrolipoamide S Acetyltransferase, Dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex), Dihydrolipoamide S-Acetyltransferase, Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex mitochondrial, DLAT, DLTA, E2, E2 component of pyruvate dehydrogenase complex, EC 2.3.1.12, M2 antigen complex 70 kDa subunit, M2 Antigen Complex 70kD Subunit, mitochondrial, ODP2_HUMAN, PBC, PDC E2, PDC-E2, PDCE2, Pyruvate dehydrogenase complex component E2, Pyruvate dehydrogenase complex E2 subunit, S acetyltransferase component of pyruvate dehydrogenase complex.
The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). It contains multiple copies of three enzymatic components: pyruvate dehydrogenase (E1), dihydrolipoamide acetyltransferase (E2) and lipoamide dehydrogenase (E3).