FH Polyclonal Antibody, Unconjugated, Rabbit
Catalog Number:
BSS-BS-3938R
Product Overview
Article Name:
FH Polyclonal Antibody, Unconjugated, Rabbit
Biozol Catalog Number:
BSS-BS-3938R
Supplier Catalog Number:
bs-3938R
Alternative Catalog Number:
BSS-BS-3938R-100
Manufacturer:
Bioss
Host:
Rabbit
Category:
Antikörper
Application:
ELISA, IF, IHC-Fr, IHC-P
Species Reactivity:
Mouse, Rat
Conjugation:
Unconjugated
Alternative Names:
mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.
Product Description
Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
Product Properties
Clonality:
Polyclonal
Concentration:
1ug/ul
NCBI:
2271
Buffer:
0.01M TBS(pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
Source:
KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
Target:
FH
Application Notes
Application Dilute:
ELISA(1:500-1000), IHC-P(1:200-400), IHC-F(1:100-500), IF(IHC-P)(1:50-200), IF(IHC-F)(1:50-200), IF(ICC)(1:50-200)
