FH Polyclonal Antibody, RBITC Conjugated, Rabbit

Product Overview

• Article Name: FH Polyclonal Antibody, RBITC Conjugated, Rabbit
• Biozol Catalog Number: BSS-BS-3938R-RBITC
• Supplier Catalog Number: bs-3938R-RBITC
• Alternative Catalog Number: BSS-BS-3938R-RBITC-100
• Manufacturer: Bioss
• Host: Rabbit
• Category: Antikörper
• Application: IF
• Species Reactivity: Mouse, Rat
• Conjugation: RBITC
• Alternative Names: mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.

Product Description

Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.

Product Properties

• Clonality: Polyclonal
• Concentration: 1ug/ul
• NCBI: 2271
• Buffer: Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
• Source: KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
• Target: FH

Application Notes

• Application Dilute: IF(IHC-P)(1:50-200), IF(IHC-F)(1:50-200), IF(ICC)(1:50-200)