Recombinant mouse ACOX1 protein, C-His, Unconjugated

Product Overview

• Article Name: Recombinant mouse ACOX1 protein, C-His, Unconjugated
• Biozol Catalog Number: BSS-BS-42132P
• Supplier Catalog Number: bs-42132P
• Alternative Catalog Number: BSS-BS-42132P-100,BSS-BS-42132P-500
• Manufacturer: Bioss
• Category: Proteine/Peptide
• Species Reactivity: Other
• Conjugation: Unconjugated

Product Description

Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD), also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.

Product Properties

• Tag: C-His
• NCBI: 11430
• UniProt: Q9R0H0
• Buffer: 20mM Tris-HCl (pH8.0)with 8M Urea.
• Source: Recombinant mouse ACOX1 protein is expressed in E.coli with C-His. It contains the amino acid sequence of 386-661/661
• Expression System: E.coli
• Purity: > 90% as determined by SDS- PAGE