2-Hydroxy-3-methylbutyric acid, CAS [[4026-18-0]] Preis auf Anfrage

Catalog Number: BYT-ORB1221132
Article Name: 2-Hydroxy-3-methylbutyric acid, CAS [[4026-18-0]] Preis auf Anfrage
Biozol Catalog Number: BYT-ORB1221132
Supplier Catalog Number: orb1221132
Alternative Catalog Number: BYT-ORB1221132-1,BYT-ORB1221132-500,BYT-ORB1221132-200,BYT-ORB1221132-100
Manufacturer: Biorbyt
Category: Biochemikalien
2-Hydroxy-3-methylbutyric acid (2-hydroxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria methylmalonic acidemia propionic acidemia 3-ketothiolase deficiency isovaleric acidemia 3-methylcrotonylglycemia 3-hydroxy-3-methylglutaric acidemia multiple carboxylase deficiency glutaric aciduria ornithine transcarbamylase deficiency glyceroluria tyrosinemia type I galactosemia and maple syrup urine disease.
Molecular Weight: 118.1
Purity: >98% (HPLC)
CAS Number: [4026-18-0]
Formula: C5H10O3
Target: Others