Recombinant Frataxin (Mitochondrial Marker) Antibody, IgG1, Clone: [rFXN/2124], Mouse, Monoclonal

Product Overview

• Article Name: Recombinant Frataxin (Mitochondrial Marker) Antibody, IgG1, Clone: [rFXN/2124], Mouse, Monoclonal
• Biozol Catalog Number: NBT-2395-MSM6-P1ABX
• Supplier Catalog Number: 2395-MSM6-P1ABX
• Alternative Catalog Number: NBT-2395-MSM6-P1ABX-100
• Manufacturer: NeoBiotechnologies
• Host: Mouse
• Category: Antikörper
• Application: ELISA
• Species Reactivity: Human
• Immunogen: Recombinant human Frataxin protein fragment (around aa 57-210) (exact sequence is proprietary)
• Alternative Names: CyaY, d-FXN, FARR, Frataxin mature form, Frataxin (81-210), FRDA, Friedreich ataxia protein, Fxn, i-FXN, m56-FXN, m78-FXN, m81-FXN, X25

Product Description

Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreichs ataxia (FRDA), a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix suggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet.

Product Properties

• Clonality: Monoclonal
• Clone Designation: [rFXN/2124]
• Molecular Weight: 14kDa
• Isotype: IgG1
• NCBI: 2395
• UniProt: Q16595
• Form: 200ug/ml of Ab Purified from Bioreactor Concentrate by Protein A/G. Prepared in 10mM PBS with 0.05% BSA & 0.05% azide. Also available WITHOUT BSA & azide at 1.0mg/ml.
• Antibody Type: Recombinant Monoclonal Antibody

Application Notes

• Application Notes: ELISA (Use Ab at 2-4ug/ml for coating) (Order Ab without BSA),Optimal dilution for a specific application should be determined.

Images

SDS-PAGE Analysis of Purified Frataxin Recombinant Mouse Monoclonal Antibody (rFXN/2124). Confirmation of Purity and Integrity of Antibody.