3beta,7beta-Dihydroxy-5-cholestenoic acid is a C27 acid whose levels are elevated in Niemann-Pick Type C and B diseases, leading to toxicity in ocular motor neurons. It is synthesized by the enzymatic action of hydroxysteroid 11-beta dehydrogenase 1 from 3beta-hydroxy-7-oxocholest-5-en-(25R)26-enoic acid (3betaH,7O-CA).
Molecular Weight:
432.64
CAS Number:
[1246298-66-7]
Formula:
C27H44O4
Target:
Endogenous Metabolite|||Others
T201321
* VAT and and shipping costs not included. Errors and price changes excepted