BBOX1 Protein, Human, Recombinant (His & GST)

Product Overview

• Article Name: BBOX1 Protein, Human, Recombinant (His & GST)
• Biozol Catalog Number: TGM-TMPY-03756
• Supplier Catalog Number: TMPY-03756
• Alternative Catalog Number: TGM-TMPY-03756-5UG, TGM-TMPY-03756-10UG, TGM-TMPY-03756-20UG, TGM-TMPY-03756-50UG, TGM-TMPY-03756-100UG
• Manufacturer: TargetMol
• Category: Biochemikalien
• Alternative Names: gamma-BBH , gamma-BBH , butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1 , BBOX , butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1 , butyrobetaine (gamma), 2-oxoglutarate dioxygenase (gamma-butyrobetaine hydroxylase) 1 , BBH , G-BBH

Product Description

BBOX1, also known as gamma-BBH, belongs to thegamma-BBH/TMLD family. It is highly expressed in kidney and moderately expressed in liver. BBOX1 catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. BBOX1 is an inhibition target for mildronate which can be used to treatanginaandmyocardial infarction. Mildronate may also be beneficial for the treatment ofneurological disorder,diabetes, andseizures andalcohol intoxication.

Images

TMPY-03756