OPA3 (Optic Atrophy 3 Protein, Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia)), Rabbit

Catalog Number: USB-487550
Article Name: OPA3 (Optic Atrophy 3 Protein, Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia)), Rabbit
Biozol Catalog Number: USB-487550
Supplier Catalog Number: 487550
Alternative Catalog Number: USB-487550-100
Manufacturer: US Biological
Host: Rabbit
Category: Antikörper
Application: WB
Immunogen: Synthetic peptide corresponding to the C-terminal region of human OPA3
The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene. Applications: Suitable for use in Western Blot. Other applications not tested. Recommended Dilution: Optimal dilutions to be determined by the researcher. Storage and Stability: May be stored at 4C for short-term only. Aliquot to avoid repeated freezing and thawing. Store at -20C. Aliquots are stable for 12 months after receipt. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap.
NCBI: 001017989
UniProt: Q9H6K4
Purity: Purified by affinity chromatography.
Form: Supplied as a liquid in PBS, 2% sucrose, 0.09% sodium azide.